Excludes

  1. Endocrine, nutritional and metabolic diseases (E00-E89)

    Type 1transitory endocrine and metabolic disorders specific to newborn (P70-P74)

  2. Metabolic disorders (E70-E88)

    Type 1androgen insensitivity syndrome (E34.5-)

    Type 1congenital adrenal hyperplasia (E25.0)

    Type 1hemolytic anemias attributable to enzyme disorders (D55.-)

    Type 1Marfan syndrome (Q87.4-)

    Type 15-alpha-reductase deficiency (E29.1)

    Type 2Ehlers-Danlos syndromes (Q79.6-)

  3. Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism (E71)
  4. Peroxisomal disorders (E71.5)

    Type 1Schilder's disease (G37.0)

  5. Disorders of peroxisome biogenesis (E71.51)

    Type 1Refsum's disease (G60.1)

  6. Neonatal adrenoleukodystrophy (E71.511)

    Type 1X-linked adrenoleukodystrophy (E71.42-)