Excludes

  1. Endocrine, nutritional and metabolic diseases (E00-E89)

    Type 1transitory endocrine and metabolic disorders specific to newborn (P70-P74)

  2. Metabolic disorders (E70-E88)

    Type 1androgen insensitivity syndrome (E34.5-)

    Type 1congenital adrenal hyperplasia (E25.0)

    Type 1hemolytic anemias attributable to enzyme disorders (D55.-)

    Type 1Marfan syndrome (Q87.4-)

    Type 15-alpha-reductase deficiency (E29.1)

    Type 2Ehlers-Danlos syndromes (Q79.6-)

  3. Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism (E71)
  4. Disorders of fatty-acid metabolism (E71.3)

    Type 1peroxisomal disorders (E71.5)

    Type 1Refsum's disease (G60.1)

    Type 1Schilder's disease (G37.0)

    Type 2carnitine deficiency due to inborn error of metabolism (E71.42)

  5. Disorders of fatty-acid oxidation (E71.31)
  6. Glutaric aciduria type II (E71.313)

    Type 1glutaric aciduria (type 1) NOS (E72.3)