Excludes

  1. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

    Type 2autoimmune disease (systemic) NOS (M35.9)

    Type 2certain conditions originating in the perinatal period (P00-P96)

    Type 2complications of pregnancy, childbirth and the puerperium (O00-O9A)

    Type 2congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)

    Type 2endocrine, nutritional and metabolic diseases (E00-E88)

    Type 2human immunodeficiency virus [HIV] disease (B20)

    Type 2injury, poisoning and certain other consequences of external causes (S00-T88)

    Type 2neoplasms (C00-D49)

    Type 2symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

  2. Other disorders of blood and blood-forming organs (D70-D77)
  3. Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue (D76)

    Type 1(Abt-) Letterer-Siwe disease (C96.0)

    Type 1eosinophilic granuloma (C96.6)

    Type 1Hand-Schüller-Christian disease (C96.5)

    Type 1histiocytic medullary reticulosis (C96.9)

    Type 1histiocytic sarcoma (C96.A)

    Type 1histiocytosis X, multifocal (C96.5)

    Type 1histiocytosis X, unifocal (C96.6)

    Type 1Langerhans-cell histiocytosis, multifocal (C96.5)

    Type 1Langerhans-cell histiocytosis NOS (C96.6)

    Type 1Langerhans-cell histiocytosis, unifocal (C96.6)

    Type 1leukemic reticuloendotheliosis (C91.4-)

    Type 1lipomelanotic reticulosis (I89.8)

    Type 1malignant histiocytosis (C96.A)

    Type 1malignant reticulosis (C86.0)

    Type 1nonlipid reticuloendotheliosis (C96.0)

  4. Hemophagocytic lymphohistiocytosis (D76.1)